2. HISTORY
11 years old male child
Diagnosed to have a heart disease at the age of 6
months when he had h/o breathing difficulty
Symptoms improved after medications
One more episode of LRTI at 13 months of age
No H/o feeding difficulty, cyanotic spells , pedal
edema.
H/o failure to thrive
Born out of non consanguineous marriage, no other
member in the family having a HD
2
3. EXAMINATION
GPE: wt-16kg , ht-120cm, BMI: 11.1 kg/m2 with some
pallor, No cyanosis, jaundice, clubbing, lymphadenopathy,
pedal oedema
Vitals : B.P-110/70 mmhg ,Pulse-98/mt regular normal
volume & character no RR or RF delay , RR-20/mt ,
afebrile. JVP: Not raised
CVS:
Apex: RV type, diffuse, Grade 1/3 parasternal haeve
+nt, epigastric pulsations +nt
S1-N ; S2- Loud P2; no additional sounds;
3/6 pan systolic murmur most prominent in 3rd
and 4th
Lt ICS, high pitched , no variation with respiration
No other murmur
3
6. Situs solitus , Levocardia, Normal systemic and pulmonary
venous drainage, AV –VA concordance, NRGA
Intact IAS
Large perimembranous VSD with B/D shunt (mostly lt rt) with
IV gradient 24 mm Hg
No PDA
LA, LV are dilated, Normal right sided chambers
Mild TR with RVSP of 90 mm Hg, No AR , PR , MR
No associated PDA,COA , ASD , RVOT obs
Good biventricular function
2D - ECHO
6
7. CATHETERISATION
11 years old male child
Ht-120 cm, wt-16 kg , BMI- 13.29Kg/mt2, BSA- 0.66 mt2
Hb-8.8 gm/dl,
HR- 115/min, SpO2-100% (RA)
O2 con-151 ml/min/mt2
INDICATION: - ASSESSMENT OF PA PRESSURE
AND REVERSIBILITY OF THE SHUNT
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18. CONDITION-2 DATA
FA 88/60/75
PCWP 8
PA 76/33/56
RV 81/9
RA 9/2/5
LV 97/11
CHAMB
ER
PO2 SPO2
IVC 56.5 82.7
SVC 60.6 84.3
PA 201 99.2
LV 496 99.6
FA 465 99.6
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20. ANALYSIS
• NORMAL SYSTEMIC PRESSURE
• NORMAL LV SYSTOLIC AND FILLING PRESSURE
• NO SIGNIFICANT GRADIENT ACROSS LV TO AORTA
• HIGH SYSTOLIC, DIASTOLIC AND MEAN PA
PRESSURES
• HIGH RV SYSTOLIC PRESSURE AND NORMAL FILLING
PRESSURE
• NO SIGNIFICANT GRADIENT FROM RV TO PA
• BOTH PVRi AND PVR/SVR RATIOS DECREASED IN
CONDITION 2
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