2. Definition:
• ARMs are developmental deformities of the lower end of the alimentary tract,
i.e., the anorectal canal.
• The term imperforate anus is used to describe all congenital abnormalities of
the anorectal canal or in location of the anus within the perineum.
3. Incidence:
• Minor abnormalities of the anus and rectum occur in 1 of 500 living
newborns, while major abnormalities occur in 1 of 5000 living
infants.
6. Classification:
• Classification of ARMs can be done into three groups in the infants without a normal anus.
1. With a visible abnormal opening of the bowel:
a. Anal stenosis
b. Anoperineal fistula
c. Anovestibular fistula in female
2. With an invisible but manifested opening of the bowel:
a. Rectovaginal fistula in female
b. Rectourethral fistula in male
c. Rectovesicular fistula
3. No manifested opening of the bowel:
a. Persistent anal membrane
b. Rectal atresia
7. CONTD…..
• Anorectal malformations can be classified into two groups on the basis of levator ani muscle, which is the
main muscle of fecal control:
1. Supralevator or high anorectal malformations:
• When rectum terminates above the levator ani muscle, which is found as rectal atresia, rectoprostatic fistula
and rectovaginal fistula. About 30% of children with high ARMs or associated genitourinary fistula achieve
bowel continence.
2. Translevator or low anorectal malformations:
• When rectum terminates below the levator animuscle, e.g., in anocutaneous fistula and Anovestibular fistula.
About 90% of children with low ARMs achieve bowel incontinence.
8. Clinical Manifestations:
Absence of stool. There is no passage of stool within a day or two of
birth.
Passing of stools in other openings. The infant may pass stools
through another opening like the urethra in boys or vagina in girls.
Swollen belly. The newborn could not pass out stools, resulting in a
swollen belly.
Absence of anal opening. The opening of the anus is missing or not in
its usual place; in girls, this may be near the vagina.
9. The specific features for specific anomalies
• Imperforate Anal Membrane:
Infant fail to pass meconium. Greenish bulging membrane seen on examination.
• Anal Stenosis:
It accounts for 10% of all ARMs. The baby may pass ribbon like stools with difficulty
as the anal opening is very small.
• Anal Agenesis:
It presents with only anal dimple. Intestinal Obstruction may develop.
10. • Rectal Agenesis:
It accounts 75% of all ARMs. It presents with fistula & can observe in male baby.
• Rectoperineal fistula:
It is found in small orifice in the perineum. In male baby it is found close to the scrotum and
in female in the vulva.
• Rectovaginal Fistula:
It presents with a communication between rectum and vagina and stool passed through the
vagina.
11. Diagnostic Evaluation:
HC
PE
Laboratory Studies- CBC, Blood Typing & Screening
Sacral Radiography
Abdominal USG
X-ray with inverted infant (upside down position), i.e., invertogram or wangensteen
Rice X-ray is useful to locate rectal pouch
Urine examination
Spinal ultrasonography or MRI
Lateral pelvic radiography at 24 hours.
Micturating cystourethrogram- to detect urinary abnormalities
12. Management:
Medical Management:
Nothing per mouth
Neonatal colostomy.
Primary neonatal pull-through without colostomy.
Diet.
Activity.
Laxatives
Antibiotic Prophylaxis
15. Nursing Considerations:
Nursing Diagnosis
• Based on the assessment data the major nursing diagnoses are:
Fluid volume deficit related to excessive loss through vomiting.
Impaired skin integrity related to the colostomy.
Risk for infection related to surgical procedures.
16. Nursing Considerations:
• Nursing Interventions
• Nursing interventions for a child with imperforate anus are:
•
Avoid infection.
Protect skin integrity.
Restore balanced fluid volume.
17. Complications:
UTI
Intestinal Obstruction
Fecal impaction
Colostomy related problems
Recurrence of fistula
Anal stenosis
Postoperative complications
18. Bibiliography:
Wong’s. (2005), Essentials of Pediatric nursing, 7th Edition, Elsevier Publications, New Delhi. Page no:
883- 885.
Parul Datta. (2007), Pediatric Nursing, 4th Edition, Jaypee publications, New Delhi. Page No: 271-273.
Dorothy R. Marlow (2008), Textbook of Pediatric Nursing, 6th Edition, Elsevier publications, New Delhi.
Page No: 457-459.
Rimple sharma(2017), Essentials of Pediatric Nursing, 2nd Edition, Jaypee publications, New Delhi.
Page No: 313-317
Websites:
• https://nurseslabs.com/imperforate-anus/
• https://www.slideshare.net/VipinChandran21/anorectal-malformation-110975114