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Sickle Cell Anemia Dr. Sabir
What is Sickle Cell Anemia (SCA)? ,[object Object],[object Object],[object Object],[object Object]
Pathogenesis ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
PATHOGENESIS Arterial pO 2  oxyHbS(soluble)   Stiff,viscous sickle cell Venous pO 2  deoxyHbS polymerised) Membrane changes  Ca 2+  influx,K + leakage Capillary venule occlusion Shortened red cell survival Microinfarction Ischemic tissue pain Ischemic organic malfn. Anemia, jaundice
Mechanism -HbS ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
LAB DIAGNOSIS ,[object Object],[object Object],[object Object]
BLOOD PICTURE ,[object Object],[object Object],[object Object],[object Object],[object Object]
 
Screening ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
Early Symptoms  and Complications ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
Medical Complications ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
Serious Complications: PAIN Recurrent Pain Episodes or  Sickling Crises ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],Danger Signs of a Crisis ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],SEEK URGENT HOSPITAL TREATMENT IF IN CRISIS
Crises ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],Triggers of Pain
Alleviating Pain ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],Daily Preventive Measures
Treating Complications ,[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]
[object Object],[object Object],[object Object],[object Object],[object Object],[object Object],Developing Treatments
[object Object],[object Object],[object Object],Developing Treatments
[object Object],[object Object],[object Object],[object Object],[object Object],[object Object]

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Medicine 5th year, 8th lecture/part three (Dr. Sabir)

  • 1. Sickle Cell Anemia Dr. Sabir
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  • 4. PATHOGENESIS Arterial pO 2 oxyHbS(soluble) Stiff,viscous sickle cell Venous pO 2 deoxyHbS polymerised) Membrane changes Ca 2+ influx,K + leakage Capillary venule occlusion Shortened red cell survival Microinfarction Ischemic tissue pain Ischemic organic malfn. Anemia, jaundice
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