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DISABILITIES AND
  DEFORMITIES IN
LEPROSY PATIENTS
"Leprosy work is not merely medical
relief; it is transforming frustration
of life into joy of dedication, personal
ambition into selfless service"
                        Mahatma Gandhi
REFERENCES:-----
•   IADVL
•   IAL
•   PARK’ Preventive and Social Medicine
•   Journals
TERMINOLOGY
• `Impairments' are defined as `problems in body function
  or structure such as a significant deviation or loss'. An
  example of an impairment in body function would be
  loss of sensation; examples of impairments in body
  structure would be contractures and absorption.
• A `deformity' is a structural, usually visible, impairment.
• A `defect' could be either a functional or structural
  impairment.
• `Disability' is used as an umbrella term for impairments,
  activity limitations and participation restrictions.
Risk factors and Types Of Deformities
• Risk factors are:-
1) Type of Leprosy- more extensive and highly
   bacilliferous types carry a high risk if not treated
   early.
2) No. of nerve trunk involved- more than three
   nerve trunk involvement increases the risk
   manifold.
3) Attack of reaction and neuritis increases the risk.
4) Duration of active disases- longer the disease
   remains untreated, greater the risk of disability.
• Types of Deformities:-
Specific Deformities:-
        arise due to local infection with M.lepra like
        loss of eyebrows, nasal deformities.
        (face>hands=feet)
Paralytic Deformities:-
        result from damage to motor nerves like claw
        finger, foot drop, facial palsy.
        (hands>feet>face)
Anesthetic deformities:-
        results from insensitivity because of damage
        to sensory nerves like ulceration, mutilation.
        (feet>hands>face)
WHO Classification and Grading
HANDS AND FEET

Grade 0: no anaesthesia, no visible deformity or damage.
Grade 1: anaesthesia present, but no visible deformity or damage.
Grade 2: visible deformity or damage present.
EYES

Grade 0: no eye problem due to leprosy; no evidence of visual loss.
Grade 1: eye problems due to leprosy present, but vision not severely
affected as a result of these (vision: 6/60 or better; can count fingers at
6 m).
Grade 2: severe visual impairment (vision: worse than 6/60; inability to
count fingers at 6 m) also includes lagophthalmos, iridocyclitis and
corneal opacities.
Grade            Degree of impairment                Included                             Excluded

Hands and feet

0           No sensory impairment,         Scars of healed ulcers, when
            no visible impairment          sensation is normal
1           Sensory impairment present,    Scars of healed ulcers, when        Scars of healed ulcers when
            no visible impairment          sensation is impaired               sensation is present
                                           Hands or feet following             Minor skin cracks
                                           successful reconstructive surgery
                                           Muscle weakness without
                                           clawinga
2           Visible impairments present    Ulcers, severe cracks,
                                           severe atrophya

Eyes

0           No eye impairment; no
            visible or vision impairment
                                                                               b
1           Eye impairment present         Absence of (regular)                    Corneal sensation testing19
            (vision: > 6/60)               blink
2           Severe visual impairment       Unable to count ®ngers at 6 m       Facial impairments due to
            (vision: < 6/60)               Lagophthalmos                       lepromatous leprosyc
                                                                               Corneal opacities, uveitis19
Nerve Involvement
• Nerve damage occurs in two settings-
     in skin lesion– small dermal sensory and
autonomic nerve fibres supplying dermal and
subcutaneous structures are damaged.
     involving Peripheral nerve trunks– usually those
which are superficial or are in fibrocasseous tunnels
leading to dermato sensory loss and dysfunction of
muscles.
• Nerve involvement in leprosy can be said to occur in
  5 stages:--
  First two are recognized histologically while next
three by clinical examination
Stages                         Charecteristics

1 Parasitization               A few leprae found in nerve

2 Tissue response              Host tissue response(TT to LL)+, bacilli+

3 Clinical involvement         Clinically thickened w or w/o pain. No NFD

4 Nerve damage                 NFD+, recovery possible

5 Nerve destruction            Irreversible NFD, severe wasting +



 Posterior tibial nerve is the most frequently affected nerve
   followed by ulnar, median, lateral popliteal and facial.
Nerve Care Practice
• AIM- to prevent permanent damage to nerve trunks
• It involves-
    Recognizing acute or subacute “clinical neuritis”
    and treating it using steroid or other measures.
    Recognizing nerve function defect and instituting
     appropriate treatment without delay.

‘Clinical neuritis’ is diagnosed when a nerve trunk shows
moderate to severe nerve pain. It may or may not be
associated with NFD and similarly NFD may or may not be
associated with clinical neuritis(Quiet Nerve Paralysis)
NERVE TENDERNESS SCALE-
GRADE                                     Clinical features
0                No tenderness            Palpation not poanful
1                Mild tenderness          Palpation hurts only when asked about it


2                Moderate tenderness      Palpation hurts even w/o asking


3                Severe tenderness        Palpation is very painful
4                Very severe tenderness   Pt. is apprehensive of palpation



Categorization of pt. acc. To NFD and Clinical Neuritis-
    Nerve Function Deficit                           Clinical Neuritis
                                          Absent                         Present

    Absent                                 A                                 B

    Present                                C                                 D
• Category A patients-
      pt is taught how to look for signs and symptoms of
neuritis.
• Category B patients-(Neuritis +, no NFD)
     Start Prednisolone 40-80 mg daily          4 wks
     taper dose 5mg/wk upto 30mg            2-3 wks
     and then taper it.
• In BT leprosy cases(neuritis due to RR), if there is no
  significant improvement in the clinical condition
  within 48-72 hrs then immediate surgical
  decompression is required so that haemperfusion to
  nerve can occur.
• In BL and LL cases(neuritis due to ENL), one can wait
  for six weeks or even longer
• Category C patients- ( No neuritis,NFD+)
    Clinically, one may assume that the nerve trunk
has the potential to recover if NFD is :-
• of recent onset - < 6 mnths involvement
• incomplete- some sensibility is there
• and if no severe muscle wasting present
    If NFD considered reversible:-
        prednisolone 30mg        4 wks
        then tapered off over 30 days.
    If NFD not recent:-
         prevent secondary impairement.
• Category D patients:-(NFD +, neuritis+)
     Prednisolone 40-80 mg daily       2-3 wks
                            reduce to maintenance dose in 3-4wks

      Maintenance dose 30mg daily                 8-10 wks

If there is no improvement in neuritis within 3-7days
then surgical decompression is required.
To accelerate resolution of inflammation:-
   1- splint affected nerve in slightly stretched position
   2-supportive therapy like analgesics
   3- short wave or microwave diathermy
• Nerve abscess is cold abscess occuring in a
  damaged fascicle usually in Tuberculoid Leprosy
• Ocassionaly, ‘hot’ abscess occurs in ENL related
  neuritis
   Management :--
• if nerve shows no NFD: wait and watch, drain
  abscess only if risk of sinus formation is there.
• if nerve is considered irrecoverably damaged:
  same as above.
• if NFD is considered likely to recover: evacuate
  and excise the abscess.
Hand Problems in Leprosy Patients
• Hands are affected because of damage to nerves
  supplying them or directly affected by reactional
  process(especially in BL, LL).
• Ulnar nerve is affected most often than others.
• In BL,LL cases usually Glove type extensive acral
  anesthesia occurs without significant motor
  involvement.
• Therefore loss of sensibility in palm doesn’t
  necessarily indicate damage to nerve trunk, as it may
  also result from destruction of dermal nerve twigs.
• Muscle weakness is sure sign of damage of nerve
  trunk.
Impairement                 Direct consequences         Late consequences

Damage to somatic sensory   Loss of sensibility         Anesthetic
fibres                                                  deformities(ulcers,shortening
                                                        of digits.)


Damage to motor fibres      Muscle paralysis            Contracture

Damage to sudomotor         Dry skin                    Deep cracks, hand infections
autonomic fibres


Lepra reaction              Inflammatory odema,         Severe fixed
                            osteoporosis, bone          deformities(specific
                            destruction, pathological   deformities,bizzare
                            fractures                   deformities)
Sensory loss leads to:-
  Loss of perception of pain and heat deprives the
  hand of its protective mechanism.
  Motor activities become clumsy and difficult
  because muscle action is not fine tuned.
  Frequently injuries results in anesthetic
  deformities(shortening of digits).
Dryness of Palmar skin :-
  Lack of sweating
  Cracks at digital creases
• Care of Insensitive Hand:-
    Skin care practices:-
           daily soaking hands in water for 15 min.
           rubbing palms vigorously
           apply liquid parrafin or vegetable oil
    Injury care practices:-
           precaution against burns while cooking
           using utensils with insulated handles
           daily inspection of hands
           using bulky bandages in case injury occurs
• Paralytic deformities of hand:-
ulnar nerve supplies--- flexor carpi ulnaris
                     medial half of flexor digitorum
                   hypothenar muscles
                  adductor pollicis and all interossei
                  medial two lumbricals
median nerve supplies:--all flexor muscles of forearm
                     thenar muscles
                     first two lumbricals
• Ulnar palsy leads to:-
      Ulnar claw hand(hyper extended MCP and flexed PIP jts)
       Loss of adduction and abduction
• Combined Ulnar and Median nerve palsy:-
      all intrinsic muscles are paralysed
      complete claw hand
      handling of objects become very difficult
Corrective Surgery are:--
  Lasso insertion
  Zancolli’s operation               augment flexion forces at MCP jt
  Srinivasan’s operation
  Bunnell’s
  Brand                          augments extension forces at PIP jt
  Antia
• Specific Deformities of hand:-
    Banana Fingers       (due to heavy infiltration)
    Shortening of fingers (due to resorption and fragmentation)
    “Reaction Hand”     (when hand is involved in reactional states)
        Foci of ac. Inflammation develops which
        eventually resolves with dense fibrosis.
       Foci may be located in dorsal skin, s/c adipose
        tissue, in small muscles or in small bones.
       Lession in interossei leads to Swan Neck deformity.
      Rx.
       Start systemic corticosteroids therapy(30 mg),
      Initially hand is rested using splint in functional position
       Wax baths
      Active movements after subsidising acute phase
Massage and Exercises for Hands:-
• Massage :- it should be done gently, after applying
        oil, place hand and gently stroke it with other.
• Exercise :-
     press hand(flexed at MCP) against thigh and open flexed
      fingers with other hand
      take a soft rubber ball for squeezing
      in recent onset deformity, splints should be used.
Four main types of splints are used:-( delivered by H Workers)
        Adductor Band splint(in splayed fingers)
        Finger Loop Splint(maintain lumbricals in position and
                            strengthen small muscles of hand)
        Opponens Loop Splint
        Gutter Splint(in late cases with stiffness)
Adductor          Finger loop        Gutter splint




Opponens loop
Grip Aids:--used after advanced deformities like
            absorption and amputation.
 Epoxy resins Grip Aids- applied on articles of work
 Instant Grip aid kit- immediate benefit in daily work
Foot Problem In Leprosy Patients
• Common problems are:-
           Plantar ulceration
            Foot drop
            Fixed deformities of feet and toes
           Tarsal disorganisation.
PLANTAR ULCERATION:--
   found in 10% of patients
   manifestation of sensorimotor deficit
   mostly in front part of sole in MTP joint
   augmented by infection through fissures and paralysis
   of feet muscles(which counter the stress while walking)
• Stages and Types of feet ulcers:
     Stages---
  First stage – threatened ulceration(dorsal puffiness, deep
                                               tenderness)
  Second stage – concealed ulceration(destruction of soft
                                                  tissue has occurred)
  Third stage – open ulceration(necrosis blister open and exposed)

     Types---
  Acute ulcer– frankly infected, purulent, covered with slough
  Chronis ulcer– indolent ulcer with hyperkeratotic edges,
                     covered with granulation tissue
  Complicating ulcer– infection spread to deeper structure
                          may lead to muscle paralysis, gas gangrene,
                          tetnus or septicemia.
Management and Prevention
• Management:--
      absolute bed rest and elevate foot
      eusol bath, irrigation, dressing
      remove slough or other draining procedures
      start antibiotics
      protective foot wearing
• Prevention:--
  Protective footwear:-(type depends on state of foot)
    Feet with only sensory loss(no muscle paralysis), footwer
    should have tough outer sole, should not rub against
    toes. Eg using automobile tyre side pieces.
• Any footwear can reduce the pressure upto 25%
• Appropriate footwear should have outer sole of
  15-18mm thick and soft inner sole 18-22mm.
• Iron nails and buckles are to be avoided.
• Raja Model is most suitable one.




•
                          learn to take short steps
• Gjhh




Female models   Male models
Insensitive feet(with intrinsic muscle paralysis):-
    these require a resilient, non collapsing, shock absorbing
    insole that will dampen the impact during walking
    Microcellular rubber is most suitable.
In certain case where greater reduction of pressure is
required; add metatarsal bar obliquely or molding the
insole so that pressure can be distributed evenly over
entire plantar surface.
   Certain orthosis like fixed ankle brace can also be used
that may transfer a part of load to leg.
 Foot Care Practices:-- similar to those done for hand
       soaking, scrubbing and smearing routinely
       corn and callosities are removed carefully
       identify ‘safe limits’ of walking
• Foot drop:--
    About 1-2% of leprosy patients develop due to
damage to lateral popliteal nerve.
   Paralysis of anterior muscles give rise to foot drop
   characteristic ‘stepping gait’ occurs in which
    ball of foot instead of heel hits the ground
   inversion foot leads to overloading on outer part.

If paralysis is recent; manage under ‘Nerve Care’
therapy.
If paralysis is of >1 year duration; it is satisfactorily
corrected by anterior transposition of tibialis posterior
tendon(Srinivasan’ operation)
If surgical intervention is contraindicated; foot drop
appliances like strap, stops or springs are used that hold
foot at right angle.
• Splinting of knee:- fig. 36.10
    this allows rest to inflamed nerve and result in
quicker healing.
• Droped foot should be supported to hasten
  recovery.                Splint




• Stretching calf muscles: as in foot drop these are
  not used while walking so contracture may develop.
CONTRACTURES WITH ‘FOOT DROP’ IS TO STRETCH
THE HEEL CORDS BY LEANING FORWARD AGAINST A
WALL OR BY SQUATTING WITH HEELS ON THE
GROUND
Deformities of Face
• Most of deformities on face occurs due to infilteration
  of facial skin but paralytic deformities can also occur(in
  borderline leprosy).
• Deformities are:--
    loss of eyebrows(madarosis)
    mega lobules of ear(Budhha ear)
   premature senility(strecthing of skin due to heavy
    infiltration lead to loss of elastic tissue, when
    infiltration regresses skin become redundant)
    Sunken Nose (due to infilteration in nasal mucosa
   in LL , granuloma formed erodes the supporting
   bony structure of nose).
Eye Problem
• More commonly in BL and LL type leprosy.
• Occurs due to:-
    Direct invasion- leprous conjuctivitis, scleritis and
                      choroidal nodule.
    Acute iridocyclitis- due to immune complex deposition
    Damage to – facial nerve
                 paralysis of eyelid muscles and lagophthalmos
                - trigeminal nerve
                 loss of corneal sensation leads to exposure keratitis
                 and corneal ulceration.
Management- using spectacles,gogles or eyeshades.
            artificial tears and cover eyes during sleep
            treating ac iridocyclitis using topical corticosteroids
            surgical intervention for lagophthalmos or cataract
• Splint in facial palsy-
      use adhesive tape strips so that lower lid is not
  sagging due to gravity and angle of mouth isnt deviated




• Gynecomastia: embarrassing enlargement of breast
     in males, usually bilateral due to hormonal
     imbalances because of testicular and liver damage.
GPAS(Green Pastures Activity Scale):-
• It assess the daily routine of patients
• Can help the nurse to pick up early deformity
Daily activities are assessed as   Interpersonal relationship   For use of assistive devices



4. Not difficult                   4. No problem                4. Not necessary

3.A bit difficult                  3. Some problem 3. Not difficult

2. Very difficult                  2. More problem 2. Difficult

1. Impossible                      1. No relation               1. Very difficult
Economic Rehabilitation
• Social ostracism is now on decrease following
  extensive education about leprosy.
• Appropriate economic rehabilitation is provided eg
  sewing machines,handcrafts, carpentry ,etc.
• CBR(community based rehabilitation) aims to
  overcome activity limitation and participation
  restriction and thus improving QOL for disabled.
• WHO has endorsed the goal of reducing grade2
  disabilities by 35% from baseline of2010
Sc
Disabilities and deformities in leprosy patients and management

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Disabilities and deformities in leprosy patients and management

  • 1. DISABILITIES AND DEFORMITIES IN LEPROSY PATIENTS
  • 2. "Leprosy work is not merely medical relief; it is transforming frustration of life into joy of dedication, personal ambition into selfless service" Mahatma Gandhi
  • 3. REFERENCES:----- • IADVL • IAL • PARK’ Preventive and Social Medicine • Journals
  • 4. TERMINOLOGY • `Impairments' are defined as `problems in body function or structure such as a significant deviation or loss'. An example of an impairment in body function would be loss of sensation; examples of impairments in body structure would be contractures and absorption. • A `deformity' is a structural, usually visible, impairment. • A `defect' could be either a functional or structural impairment. • `Disability' is used as an umbrella term for impairments, activity limitations and participation restrictions.
  • 5. Risk factors and Types Of Deformities • Risk factors are:- 1) Type of Leprosy- more extensive and highly bacilliferous types carry a high risk if not treated early. 2) No. of nerve trunk involved- more than three nerve trunk involvement increases the risk manifold. 3) Attack of reaction and neuritis increases the risk. 4) Duration of active disases- longer the disease remains untreated, greater the risk of disability.
  • 6. • Types of Deformities:- Specific Deformities:- arise due to local infection with M.lepra like loss of eyebrows, nasal deformities. (face>hands=feet) Paralytic Deformities:- result from damage to motor nerves like claw finger, foot drop, facial palsy. (hands>feet>face) Anesthetic deformities:- results from insensitivity because of damage to sensory nerves like ulceration, mutilation. (feet>hands>face)
  • 7. WHO Classification and Grading HANDS AND FEET Grade 0: no anaesthesia, no visible deformity or damage. Grade 1: anaesthesia present, but no visible deformity or damage. Grade 2: visible deformity or damage present. EYES Grade 0: no eye problem due to leprosy; no evidence of visual loss. Grade 1: eye problems due to leprosy present, but vision not severely affected as a result of these (vision: 6/60 or better; can count fingers at 6 m). Grade 2: severe visual impairment (vision: worse than 6/60; inability to count fingers at 6 m) also includes lagophthalmos, iridocyclitis and corneal opacities.
  • 8. Grade Degree of impairment Included Excluded Hands and feet 0 No sensory impairment, Scars of healed ulcers, when no visible impairment sensation is normal 1 Sensory impairment present, Scars of healed ulcers, when Scars of healed ulcers when no visible impairment sensation is impaired sensation is present Hands or feet following Minor skin cracks successful reconstructive surgery Muscle weakness without clawinga 2 Visible impairments present Ulcers, severe cracks, severe atrophya Eyes 0 No eye impairment; no visible or vision impairment b 1 Eye impairment present Absence of (regular) Corneal sensation testing19 (vision: > 6/60) blink 2 Severe visual impairment Unable to count ®ngers at 6 m Facial impairments due to (vision: < 6/60) Lagophthalmos lepromatous leprosyc Corneal opacities, uveitis19
  • 9. Nerve Involvement • Nerve damage occurs in two settings- in skin lesion– small dermal sensory and autonomic nerve fibres supplying dermal and subcutaneous structures are damaged. involving Peripheral nerve trunks– usually those which are superficial or are in fibrocasseous tunnels leading to dermato sensory loss and dysfunction of muscles. • Nerve involvement in leprosy can be said to occur in 5 stages:-- First two are recognized histologically while next three by clinical examination
  • 10. Stages Charecteristics 1 Parasitization A few leprae found in nerve 2 Tissue response Host tissue response(TT to LL)+, bacilli+ 3 Clinical involvement Clinically thickened w or w/o pain. No NFD 4 Nerve damage NFD+, recovery possible 5 Nerve destruction Irreversible NFD, severe wasting + Posterior tibial nerve is the most frequently affected nerve followed by ulnar, median, lateral popliteal and facial.
  • 11. Nerve Care Practice • AIM- to prevent permanent damage to nerve trunks • It involves- Recognizing acute or subacute “clinical neuritis” and treating it using steroid or other measures. Recognizing nerve function defect and instituting appropriate treatment without delay. ‘Clinical neuritis’ is diagnosed when a nerve trunk shows moderate to severe nerve pain. It may or may not be associated with NFD and similarly NFD may or may not be associated with clinical neuritis(Quiet Nerve Paralysis)
  • 12. NERVE TENDERNESS SCALE- GRADE Clinical features 0 No tenderness Palpation not poanful 1 Mild tenderness Palpation hurts only when asked about it 2 Moderate tenderness Palpation hurts even w/o asking 3 Severe tenderness Palpation is very painful 4 Very severe tenderness Pt. is apprehensive of palpation Categorization of pt. acc. To NFD and Clinical Neuritis- Nerve Function Deficit Clinical Neuritis Absent Present Absent A B Present C D
  • 13. • Category A patients- pt is taught how to look for signs and symptoms of neuritis. • Category B patients-(Neuritis +, no NFD) Start Prednisolone 40-80 mg daily 4 wks taper dose 5mg/wk upto 30mg 2-3 wks and then taper it. • In BT leprosy cases(neuritis due to RR), if there is no significant improvement in the clinical condition within 48-72 hrs then immediate surgical decompression is required so that haemperfusion to nerve can occur. • In BL and LL cases(neuritis due to ENL), one can wait for six weeks or even longer
  • 14. • Category C patients- ( No neuritis,NFD+) Clinically, one may assume that the nerve trunk has the potential to recover if NFD is :- • of recent onset - < 6 mnths involvement • incomplete- some sensibility is there • and if no severe muscle wasting present If NFD considered reversible:- prednisolone 30mg 4 wks then tapered off over 30 days. If NFD not recent:- prevent secondary impairement.
  • 15. • Category D patients:-(NFD +, neuritis+) Prednisolone 40-80 mg daily 2-3 wks reduce to maintenance dose in 3-4wks Maintenance dose 30mg daily 8-10 wks If there is no improvement in neuritis within 3-7days then surgical decompression is required. To accelerate resolution of inflammation:- 1- splint affected nerve in slightly stretched position 2-supportive therapy like analgesics 3- short wave or microwave diathermy
  • 16. • Nerve abscess is cold abscess occuring in a damaged fascicle usually in Tuberculoid Leprosy • Ocassionaly, ‘hot’ abscess occurs in ENL related neuritis Management :-- • if nerve shows no NFD: wait and watch, drain abscess only if risk of sinus formation is there. • if nerve is considered irrecoverably damaged: same as above. • if NFD is considered likely to recover: evacuate and excise the abscess.
  • 17. Hand Problems in Leprosy Patients • Hands are affected because of damage to nerves supplying them or directly affected by reactional process(especially in BL, LL). • Ulnar nerve is affected most often than others. • In BL,LL cases usually Glove type extensive acral anesthesia occurs without significant motor involvement. • Therefore loss of sensibility in palm doesn’t necessarily indicate damage to nerve trunk, as it may also result from destruction of dermal nerve twigs. • Muscle weakness is sure sign of damage of nerve trunk.
  • 18. Impairement Direct consequences Late consequences Damage to somatic sensory Loss of sensibility Anesthetic fibres deformities(ulcers,shortening of digits.) Damage to motor fibres Muscle paralysis Contracture Damage to sudomotor Dry skin Deep cracks, hand infections autonomic fibres Lepra reaction Inflammatory odema, Severe fixed osteoporosis, bone deformities(specific destruction, pathological deformities,bizzare fractures deformities)
  • 19. Sensory loss leads to:- Loss of perception of pain and heat deprives the hand of its protective mechanism. Motor activities become clumsy and difficult because muscle action is not fine tuned. Frequently injuries results in anesthetic deformities(shortening of digits). Dryness of Palmar skin :- Lack of sweating Cracks at digital creases
  • 20. • Care of Insensitive Hand:- Skin care practices:- daily soaking hands in water for 15 min. rubbing palms vigorously apply liquid parrafin or vegetable oil Injury care practices:- precaution against burns while cooking using utensils with insulated handles daily inspection of hands using bulky bandages in case injury occurs
  • 21. • Paralytic deformities of hand:- ulnar nerve supplies--- flexor carpi ulnaris medial half of flexor digitorum hypothenar muscles adductor pollicis and all interossei medial two lumbricals median nerve supplies:--all flexor muscles of forearm thenar muscles first two lumbricals
  • 22. • Ulnar palsy leads to:- Ulnar claw hand(hyper extended MCP and flexed PIP jts) Loss of adduction and abduction • Combined Ulnar and Median nerve palsy:- all intrinsic muscles are paralysed complete claw hand handling of objects become very difficult Corrective Surgery are:-- Lasso insertion Zancolli’s operation augment flexion forces at MCP jt Srinivasan’s operation Bunnell’s Brand augments extension forces at PIP jt Antia
  • 23. • Specific Deformities of hand:- Banana Fingers (due to heavy infiltration) Shortening of fingers (due to resorption and fragmentation) “Reaction Hand” (when hand is involved in reactional states) Foci of ac. Inflammation develops which eventually resolves with dense fibrosis. Foci may be located in dorsal skin, s/c adipose tissue, in small muscles or in small bones. Lession in interossei leads to Swan Neck deformity. Rx. Start systemic corticosteroids therapy(30 mg), Initially hand is rested using splint in functional position Wax baths Active movements after subsidising acute phase
  • 24. Massage and Exercises for Hands:- • Massage :- it should be done gently, after applying oil, place hand and gently stroke it with other. • Exercise :- press hand(flexed at MCP) against thigh and open flexed fingers with other hand take a soft rubber ball for squeezing in recent onset deformity, splints should be used. Four main types of splints are used:-( delivered by H Workers) Adductor Band splint(in splayed fingers) Finger Loop Splint(maintain lumbricals in position and strengthen small muscles of hand) Opponens Loop Splint Gutter Splint(in late cases with stiffness)
  • 25. Adductor Finger loop Gutter splint Opponens loop Grip Aids:--used after advanced deformities like absorption and amputation. Epoxy resins Grip Aids- applied on articles of work Instant Grip aid kit- immediate benefit in daily work
  • 26. Foot Problem In Leprosy Patients • Common problems are:- Plantar ulceration Foot drop Fixed deformities of feet and toes Tarsal disorganisation. PLANTAR ULCERATION:-- found in 10% of patients manifestation of sensorimotor deficit mostly in front part of sole in MTP joint augmented by infection through fissures and paralysis of feet muscles(which counter the stress while walking)
  • 27. • Stages and Types of feet ulcers: Stages--- First stage – threatened ulceration(dorsal puffiness, deep tenderness) Second stage – concealed ulceration(destruction of soft tissue has occurred) Third stage – open ulceration(necrosis blister open and exposed) Types--- Acute ulcer– frankly infected, purulent, covered with slough Chronis ulcer– indolent ulcer with hyperkeratotic edges, covered with granulation tissue Complicating ulcer– infection spread to deeper structure may lead to muscle paralysis, gas gangrene, tetnus or septicemia.
  • 28. Management and Prevention • Management:-- absolute bed rest and elevate foot eusol bath, irrigation, dressing remove slough or other draining procedures start antibiotics protective foot wearing • Prevention:-- Protective footwear:-(type depends on state of foot) Feet with only sensory loss(no muscle paralysis), footwer should have tough outer sole, should not rub against toes. Eg using automobile tyre side pieces.
  • 29. • Any footwear can reduce the pressure upto 25% • Appropriate footwear should have outer sole of 15-18mm thick and soft inner sole 18-22mm. • Iron nails and buckles are to be avoided. • Raja Model is most suitable one. • learn to take short steps
  • 30. • Gjhh Female models Male models
  • 31. Insensitive feet(with intrinsic muscle paralysis):- these require a resilient, non collapsing, shock absorbing insole that will dampen the impact during walking Microcellular rubber is most suitable. In certain case where greater reduction of pressure is required; add metatarsal bar obliquely or molding the insole so that pressure can be distributed evenly over entire plantar surface. Certain orthosis like fixed ankle brace can also be used that may transfer a part of load to leg. Foot Care Practices:-- similar to those done for hand soaking, scrubbing and smearing routinely corn and callosities are removed carefully identify ‘safe limits’ of walking
  • 32. • Foot drop:-- About 1-2% of leprosy patients develop due to damage to lateral popliteal nerve. Paralysis of anterior muscles give rise to foot drop characteristic ‘stepping gait’ occurs in which ball of foot instead of heel hits the ground inversion foot leads to overloading on outer part. If paralysis is recent; manage under ‘Nerve Care’ therapy. If paralysis is of >1 year duration; it is satisfactorily corrected by anterior transposition of tibialis posterior tendon(Srinivasan’ operation) If surgical intervention is contraindicated; foot drop appliances like strap, stops or springs are used that hold foot at right angle.
  • 33. • Splinting of knee:- fig. 36.10 this allows rest to inflamed nerve and result in quicker healing. • Droped foot should be supported to hasten recovery. Splint • Stretching calf muscles: as in foot drop these are not used while walking so contracture may develop.
  • 34. CONTRACTURES WITH ‘FOOT DROP’ IS TO STRETCH THE HEEL CORDS BY LEANING FORWARD AGAINST A WALL OR BY SQUATTING WITH HEELS ON THE GROUND
  • 35. Deformities of Face • Most of deformities on face occurs due to infilteration of facial skin but paralytic deformities can also occur(in borderline leprosy). • Deformities are:-- loss of eyebrows(madarosis) mega lobules of ear(Budhha ear) premature senility(strecthing of skin due to heavy infiltration lead to loss of elastic tissue, when infiltration regresses skin become redundant) Sunken Nose (due to infilteration in nasal mucosa in LL , granuloma formed erodes the supporting bony structure of nose).
  • 36. Eye Problem • More commonly in BL and LL type leprosy. • Occurs due to:- Direct invasion- leprous conjuctivitis, scleritis and choroidal nodule. Acute iridocyclitis- due to immune complex deposition Damage to – facial nerve paralysis of eyelid muscles and lagophthalmos - trigeminal nerve loss of corneal sensation leads to exposure keratitis and corneal ulceration. Management- using spectacles,gogles or eyeshades. artificial tears and cover eyes during sleep treating ac iridocyclitis using topical corticosteroids surgical intervention for lagophthalmos or cataract
  • 37. • Splint in facial palsy- use adhesive tape strips so that lower lid is not sagging due to gravity and angle of mouth isnt deviated • Gynecomastia: embarrassing enlargement of breast in males, usually bilateral due to hormonal imbalances because of testicular and liver damage.
  • 38. GPAS(Green Pastures Activity Scale):- • It assess the daily routine of patients • Can help the nurse to pick up early deformity Daily activities are assessed as Interpersonal relationship For use of assistive devices 4. Not difficult 4. No problem 4. Not necessary 3.A bit difficult 3. Some problem 3. Not difficult 2. Very difficult 2. More problem 2. Difficult 1. Impossible 1. No relation 1. Very difficult
  • 39. Economic Rehabilitation • Social ostracism is now on decrease following extensive education about leprosy. • Appropriate economic rehabilitation is provided eg sewing machines,handcrafts, carpentry ,etc. • CBR(community based rehabilitation) aims to overcome activity limitation and participation restriction and thus improving QOL for disabled. • WHO has endorsed the goal of reducing grade2 disabilities by 35% from baseline of2010
  • 40. Sc