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CEREBRAL PALSY.pptx

  1. Syed masood
  2. DEFINITION  DISORDER OF MOVEMENT AND POSTURE DUE TO DEFECTIVE OR NON-PROGRESSIVE LESION OF IMMATURE BRAIN.
  3. EPIDEMOLOGY  1-3/1000 LIVE BIRTHS  MALES AND FEMALES ARE EQUALLY AFFECTED
  4. THE PRETERM INFANT Prof. Dr. R Harihara Prakash, MPT (Paed. Neuro) Definition by GESTATIONAL AGE BIRTH WEIGHT WHO definition: Less than 37 weeks gestation LBW: < 2500 gms VLBW: < 1500 gms ELBW: < 1000 gms Infant born before: 37 completed gestational weeks – preterm 32 completed gestational weeks – very preterm 28 completed gestational weeks – extremely preterm Lower the gestational age, more immature is the infant.
  5. ETIOLOGY 1. PEMATURITY:  TRAUMA AT DELIVERY  AFTER BIRTH DUE TO IMMATURE RESPIRATORY AND CVS 2. ASPHYXIA:  ACCIDENTS AT BIRTH  KNOTTED UMBLICAL CORD  CORD AROUND NECK  PROLAPSED CORD
  6. ETIOLOGY CONTD. 3. BIRTH TRAUMA:  DISPROPORTION  FORCEP DELIVERY  BREECH DELIVERY 4. SEVERE JAUNDICE: UNCONJUGATE BILIRUBIN IN BLOOD DEMAGES BASAL GANGLIA.
  7. ETIOLOGY CONTD. 5. HYPOGLYCEMIA: CAUSES SEVERE BRAIN DEMAGE. 6. INTRA-UTERINE VIRUS INFECTION: RUBELLA VIRUS INFECTION AND CYTOMEGALOVIRUS INFECTION. 7. NEONATAL MENINGITIS
  8. ETIOLOGY CONTD. 8. GENETIC CAUSES 9. VASCULAR CAUSES 10. CHOREOAMNIONITIS
  9. CLASSIFICATION TOPOGRAPHICAL • MONOPLEGIA • HEMIPLEGIA • DIPLEGIA • QUADRIPLEGIA ETIOLOGIC • CONGENITAL • ACQUIRED PHYSIOLOGIC • BASED ON FUNCTIONAL CLASSIFICATION.
  10. CLASSIFICATION CONTD. SYMPTOMATIC • SPASTIC • ATAXIC • ATHETOID ANATOMICAL LOCALIZATION • PYRAMIDAL • EXTRAPYRAMIDAL • CEREBELLAR
  11. HEMIPLEGIA 1. Hemiplegic children become independent walkers by age 3. 2. Sensory deficits and learning disability add to movement problem. 3. Children adopt compensatory pattern. 4. Difficulty in having midline orientation.
  12. DIPLEGIA 1. Requires walking aids. Can usually walk by the age of 4 to 7. 2. Hand dexterity is impaired. 3. Children have difficult writing and other tasks requiring fine motor control. 4. Surgery may be required for contractures and deformities.
  13. QUADRIPLEGIA 1. Mobility is major problem. 2. All four limbs are affected. 3. Poor muscle endurance. 4. Difficulty maintaining static and dynamic posture
  14. SPASTIC  DISORDER OF TONE  CAUSED BY DEMAGE TO UMN OR ALONG PATHWAYS  INCREASED DTR AND EXTENSOR PLANTER RESPONSES
  15. CONTINUES CONTRACTION OF SPASTIC MUSCLE AND APPARENT WEAKENING OF ANTAGONISTIC MUSCLE DEVELOPMENT OF DEFORMITY AT JOINT BECOME FIXED CONTRACTURES WITH TIME
  16. DIFFERENCES BETWEEN SPASTICITY AND DYSTONIA Spasticity Dystonia Examination You feel You see Tendon reflexes Increased Generally normal Clonus Present Absent Pathological reflexes Present Rare
  17. ATAXIC  CAUSED BY DEMAGE TO CEREBELLUM OR ITS PATHWAYS.  SIGNS: i. HYPOTONIA ii. DISTURBANCE OF BALANCE iii. INCORDINATION iv.INTENTION TREMORS v. DYSARTHRIA vi. NYSTAGMUS
  18. ATHETOID  DEMAGE CENTERED ON BASAL GANGLIA  IRREPRESSIBLE SLOW WRITHING MOVEMENTS.
  19. EXTRAPYRAMIDAL  CLINICAL MENIFESTATION: i. DYSKINESIA ii.DYSTONIA iii.TREMORS iv.RIGIDITY • ARMS, LEGS, NECK AND TRUNK INVOLVED • 30% OF PATIENTS • MR AND HEARING DEFICITS MAY BE PRESENT.
  20. COMMON SITES FOR CONTRACTURES Upper extremity Lower extremity Pronator Hip adductor – flexor Wrist and finger flexor Knee flexor Thumb adductor Ankle plantar flexor
  21. COMMON SITES OF DEFORMITY Place Deformity Spine Scoliosis, kyphosis Hip Subluxation, dislocation Femur and tibia Internal or external torsion Foot Equinus, valgus, varus
  22. SPINAL DEFORMITIES SPINAL DEFORMITY OCCURS IN Scoliosis Total body involved spastic and dystonia Kyphosis (thoracolumbar) Patients with no sitting balance Kyphosis (lumbar) Patients with hamstring contracture Hyperlordosis (lumbar) Ambulatory patients with hip flexion contractures
  23. SPINAL DEFORMITIES
  24. SPINAL DEFORMITIES Long C shaped hyperkyphosis in the child with weak spinal extensor muscles. Hamstring spasticity causes posterior pelvic tilt and sactal sitting resulting in lumbar kyphosis.
  25. ASSOCIATED FEATURES • OPTIC NERVE DEMAGE • CORTICAL BLINDNESS • SQUINTS VISUAL PROBLEMS • DEAFNESS AUDITORY PROBLEMS • APHASIA • DYSARTHRIA • DYSLEXIA SPEECH
  26. ASSOCIATED FEATURES • ASTEREOGNOSIS • SPATIAL DISORIENTATION SENSORY DEFICITS • DEMAGE PREVENTING DEVELOPMENT OF MEMORY MENTAL HANDICAP • GENERALIZED OR FOCALTONIC SEIZURES. SEIZURES
  27. CP IS LIKELY IF THERE IS NO 1.HEAD CONTROL AT 3 MONTHS 2.SITTING AT 6 MONTHS 3.ROLLING OVER AT 6 MONTHS 4.WALKING AT 18 MONTHS
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