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Segmental analysis of the Heart
By
Dr.M.Gibreel, FEBR, FAHC
Cardiac imaging senior Registrar
AHC & NHI
Segmental Approach
Analysis/ Evaluation of the heart in terms of segments in a step-by-step
fashion based on pattern of recognition of “normal”. Relation of the
segments to each other.
It facilitates communication between physicians from various
subspecialties who are involved in diagnosis and management of CHD.
The segments are the atria, ventricles, and great arteries
Visceroatrial situs, the ventricular loop, and the conotruncus.
The only fixed landmark is: right and left of the patient.
House Layout
• 3 floors (Major Segments)
– Viscero-atrial situs
– Ventricular loop
– Conotruncus
Or, more simply:
– Atria
– Ventricles
– Great Arteries
• 2 staircases (Segmental Connections)
– AV junction
– Conus or Infundibulum
• 2 Entrances
– Systemic veins
– Pulmonary Veins
Schools of segmental analysis
Richard Van Praagh Rob Anderson
• It was first described by Van Praagh nearly 50 years ago, in which a three-
part notation “{S, D, S}” is used as follows:
The 1st letter ….> The viscero-atrial situs
The 2nd letter ….> The ventricular looping
The 3rd letter …> The position and relation of the great vessels.
Terminology of Congenital Heart Disease
• Position.
• Situs.
• Looping.
• Concordance .
Cardiac Position = -cardia , relation of apex to
base
• Levocardia (left-sided).
• Dextrocardia (right-sided).
• Mesocardia (centrally located) within the thorax.
• Ectopia cordis (partially or completely outside the thorax).
Situs
• Situs = arrangement
• Possibilities :
1)Solitus = usual /normal . LA to the left , RA to the right.
2) Inversus = mirror the solitus . LA to the right , RA to the left.
3) ambiguus= Vague either right or left isomerism Heterotaxy
Syndromes
Hetero = “different”; -taxy = “arrangement”
Situs
• Body Segments: Atrial, Tracheo-bronchial, and Abdominal
Atrial situs “{X, , }”
•The atrial situs can usually be
established from visceral situs. In the
correct and reversed order.
•It is very rare for atrial solitus not to
reflect the visceral situs .
RA
• Appendage (triangular & wide base) + IVC.
• Crista terminalis >> ridge dividing between the
smooth part of the right atrium and the right
atrial appendage
RA
LA
• Appendage (long & narrow), trabeculations
• Rhomboid
LA
Atrial situs
Atrial morphology, arrangement and relation to each other
2 morphologically different
atriums, left atrium is to left side
and right atrium to the right side .
2 morphologically different
atriums, left atrium is to right side
and right atrium to the left side .
2 morphologically similar atriums,
2 left atria
2 right atria .
Thoraco-abdominal
situs “{X, , }”
Abdominal Situs
Tracheo-bronchial situs
Tracheo-bronchial situs
Left or right isomerism?
Left Right
IVC Interrupted continuous
CS LSVC to CS Absent CS
PV Normal to ipslateral TAPVD
IAS ASD I Common atrium
SVC Bilateral ++ Bilateral
Ventricular loop / Looping
• Defined by the rotation of the right ventricle (D-loop when the RV
seen to the right).
D-loop: RV right-sided relative to LV
L-loop: RV left-sided (levo or L) relative to LV.
RV
RV
D-loop L-loop
Ventricle
• The normal ventricle possess 3 components:
• Inlet component: the portion downstream of AV valve annlus = inflow
• Trabecualr component: body of the ventricle distal to the insertion of the
papillary muscle
• Outlet (infundibular)component : portion that supports the arterial valve of
the ventricle= outflow tract or conus.
• Continuity of inlet &outlet.
• LV in DORV is accepted to a ventricle though it has no
outlet competent.
• The minimal requirement for chamber to be considered a
ventricle are that it possess an inlet and trabecular
competent.
• Chambers which do not have an inlet portion are not
ventricles and are described as rudimentary chambers.
• Rudimentary chambers are 2 types :
 Outlet chambers , if it supplies great vessel
 Trabecular pouches, if no great vessel supplied by it .
Ventricular identification
RV
• Pyramidal shape.
• Moderator band.
• Trabeculated septal surface
• TV septal leaflet is more apical i.e. more toward the apex.
(TV predilection to septum & reverse to semilunar V.)
• Coarse trabeculations .
LV
• Oval shape
• Fine trabeculations
• Smooth septal surface, Papillary muscle.
• (Mitral V predilection to semilunar V i.e. A-M continuity , and the
reverse to the septum).
LV
LA
RA
RV
RV
D-loop L-loop
Version
• Dextroversion= situs solitus + dextrocardia.
• Levoversion = situs inversus + levocardia.
AV connections
STRADDLING
• A feature of the tensor apparatus (chordae tendineae and papillary
muscles) of an AV valve and indicates anomalous insertion into the
contralateral. ventricle, either along its septum or its free wall
Potential AV connections
AOPA
RV
LV
RA
Concordant Discordant; cc-TGA CAVC
RV
LV
RA
LA
Potential AV connections
Tricuspid atresia DILVMitral atresia
RV
LA
LV
RA
RV
LA
LV
RA
LA
LVRA
Great vessels……No isomersum
• Aorta: Arch and neck vessles , giving coronaries
• Pulmonary artery: usually bifurcates
Normal
Inversus
VA connection,,, VentriculoArterial Connection
• If Ao from LV and PA from RV: Concordant
• If Ao from RV and PA from LV: Discordant
• 3rd type of VA connection: Double outlet, almost always from RV.
• Final type of VA connection: Single outlet (truncus arteriosus).
Loop Rule
Assumption used if determination of morphologic ventricles is difficult:
• In presence of a right-sided aortic valve, the RV is to the right of the
LV (D-loop).
• In presence of a left-sided aortic valve, the RV is to the left of the LV
(L-loop).
D-TGA L-TGA
Ao PA
RV LV
AO
PA
LV
RV
Potential ventriculo-arterial connections
Potential ventriculo-arterial connections
DORV Truncus
arteriosus
Ao PA
RV
LV
PA
AO
RV
Infundibulum (conus)
• The infundibulum is part
from the RV and acts as the
connecting segment between
the ventricle and great
vessels:
• Sub-pulmonic “normal”,
• Sub-aortic “mostly in TGA”,
• Double conus “mostly in
DORV”,
• Absent conus, least common
“mostly in DOLV”.
Courtesy of Tal Geva, MD
RV
AO
RV
Ao
PA
Associated anomalies
 Venous connection
 IAS
 IVS
 Valves
 Myocardium
 Coronary anatomy
 Peripheral pulmonary arteries
 Aortic arch
Thank you

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Segmental analysis in congenital heart diseases m.gibreel

  • 1. Segmental analysis of the Heart By Dr.M.Gibreel, FEBR, FAHC Cardiac imaging senior Registrar AHC & NHI
  • 2. Segmental Approach Analysis/ Evaluation of the heart in terms of segments in a step-by-step fashion based on pattern of recognition of “normal”. Relation of the segments to each other. It facilitates communication between physicians from various subspecialties who are involved in diagnosis and management of CHD. The segments are the atria, ventricles, and great arteries Visceroatrial situs, the ventricular loop, and the conotruncus. The only fixed landmark is: right and left of the patient.
  • 3.
  • 4. House Layout • 3 floors (Major Segments) – Viscero-atrial situs – Ventricular loop – Conotruncus Or, more simply: – Atria – Ventricles – Great Arteries • 2 staircases (Segmental Connections) – AV junction – Conus or Infundibulum • 2 Entrances – Systemic veins – Pulmonary Veins
  • 5. Schools of segmental analysis Richard Van Praagh Rob Anderson
  • 6. • It was first described by Van Praagh nearly 50 years ago, in which a three- part notation “{S, D, S}” is used as follows: The 1st letter ….> The viscero-atrial situs The 2nd letter ….> The ventricular looping The 3rd letter …> The position and relation of the great vessels.
  • 7. Terminology of Congenital Heart Disease • Position. • Situs. • Looping. • Concordance .
  • 8. Cardiac Position = -cardia , relation of apex to base • Levocardia (left-sided). • Dextrocardia (right-sided). • Mesocardia (centrally located) within the thorax. • Ectopia cordis (partially or completely outside the thorax).
  • 9. Situs • Situs = arrangement • Possibilities : 1)Solitus = usual /normal . LA to the left , RA to the right. 2) Inversus = mirror the solitus . LA to the right , RA to the left. 3) ambiguus= Vague either right or left isomerism Heterotaxy Syndromes Hetero = “different”; -taxy = “arrangement”
  • 10. Situs • Body Segments: Atrial, Tracheo-bronchial, and Abdominal
  • 11. Atrial situs “{X, , }” •The atrial situs can usually be established from visceral situs. In the correct and reversed order. •It is very rare for atrial solitus not to reflect the visceral situs .
  • 12. RA • Appendage (triangular & wide base) + IVC. • Crista terminalis >> ridge dividing between the smooth part of the right atrium and the right atrial appendage
  • 13. RA
  • 14. LA • Appendage (long & narrow), trabeculations • Rhomboid
  • 15. LA
  • 16.
  • 17.
  • 19. Atrial morphology, arrangement and relation to each other 2 morphologically different atriums, left atrium is to left side and right atrium to the right side . 2 morphologically different atriums, left atrium is to right side and right atrium to the left side . 2 morphologically similar atriums, 2 left atria 2 right atria .
  • 20.
  • 22.
  • 25.
  • 27.
  • 28.
  • 29.
  • 30. Left or right isomerism? Left Right IVC Interrupted continuous CS LSVC to CS Absent CS PV Normal to ipslateral TAPVD IAS ASD I Common atrium SVC Bilateral ++ Bilateral
  • 31.
  • 32. Ventricular loop / Looping • Defined by the rotation of the right ventricle (D-loop when the RV seen to the right). D-loop: RV right-sided relative to LV L-loop: RV left-sided (levo or L) relative to LV.
  • 34. Ventricle • The normal ventricle possess 3 components: • Inlet component: the portion downstream of AV valve annlus = inflow • Trabecualr component: body of the ventricle distal to the insertion of the papillary muscle • Outlet (infundibular)component : portion that supports the arterial valve of the ventricle= outflow tract or conus. • Continuity of inlet &outlet.
  • 35. • LV in DORV is accepted to a ventricle though it has no outlet competent. • The minimal requirement for chamber to be considered a ventricle are that it possess an inlet and trabecular competent. • Chambers which do not have an inlet portion are not ventricles and are described as rudimentary chambers. • Rudimentary chambers are 2 types :  Outlet chambers , if it supplies great vessel  Trabecular pouches, if no great vessel supplied by it .
  • 36.
  • 37. Ventricular identification RV • Pyramidal shape. • Moderator band. • Trabeculated septal surface • TV septal leaflet is more apical i.e. more toward the apex. (TV predilection to septum & reverse to semilunar V.) • Coarse trabeculations .
  • 38.
  • 39. LV • Oval shape • Fine trabeculations • Smooth septal surface, Papillary muscle. • (Mitral V predilection to semilunar V i.e. A-M continuity , and the reverse to the septum).
  • 40.
  • 41. LV
  • 42.
  • 43. LA RA
  • 44.
  • 46.
  • 47.
  • 48. Version • Dextroversion= situs solitus + dextrocardia. • Levoversion = situs inversus + levocardia.
  • 49.
  • 50.
  • 52.
  • 53. STRADDLING • A feature of the tensor apparatus (chordae tendineae and papillary muscles) of an AV valve and indicates anomalous insertion into the contralateral. ventricle, either along its septum or its free wall
  • 54. Potential AV connections AOPA RV LV RA Concordant Discordant; cc-TGA CAVC RV LV RA LA
  • 55. Potential AV connections Tricuspid atresia DILVMitral atresia RV LA LV RA RV LA LV RA LA LVRA
  • 56. Great vessels……No isomersum • Aorta: Arch and neck vessles , giving coronaries • Pulmonary artery: usually bifurcates
  • 58.
  • 59.
  • 60.
  • 61. VA connection,,, VentriculoArterial Connection • If Ao from LV and PA from RV: Concordant • If Ao from RV and PA from LV: Discordant • 3rd type of VA connection: Double outlet, almost always from RV. • Final type of VA connection: Single outlet (truncus arteriosus).
  • 62.
  • 63. Loop Rule Assumption used if determination of morphologic ventricles is difficult: • In presence of a right-sided aortic valve, the RV is to the right of the LV (D-loop). • In presence of a left-sided aortic valve, the RV is to the left of the LV (L-loop).
  • 64. D-TGA L-TGA Ao PA RV LV AO PA LV RV Potential ventriculo-arterial connections
  • 65. Potential ventriculo-arterial connections DORV Truncus arteriosus Ao PA RV LV PA AO RV
  • 66. Infundibulum (conus) • The infundibulum is part from the RV and acts as the connecting segment between the ventricle and great vessels: • Sub-pulmonic “normal”, • Sub-aortic “mostly in TGA”, • Double conus “mostly in DORV”, • Absent conus, least common “mostly in DOLV”. Courtesy of Tal Geva, MD
  • 68.
  • 69.
  • 70.
  • 71. Associated anomalies  Venous connection  IAS  IVS  Valves  Myocardium  Coronary anatomy  Peripheral pulmonary arteries  Aortic arch
  • 72.
  • 73.
  • 74.
  • 75.
  • 76.

Editor's Notes

  1. Normal, inversus, Right, left isomerism
  2. D loop, L loop
  3. D loop, L loop
  4. N, CC TGA, CAVC
  5. Tricuspid atresia, mitral atresia, DILV
  6. N, situs inversus , mal-posed side by side
  7. DTGA, LTGA
  8. DORV youssef islam 5558, DOLV
  9. N, N, DTGA Aorta on conus, DORV, bilateral conus