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Coarctation of Aorta




                                             Dr. Kalpana Malla
                                            MBBS MD (Pediatrics)
                                         Manipal Teaching Hospital


Download more documents and slide shows on The Medical Post [ www.themedicalpost.net ]
Coarctation of aorta
• 8-10% of CHDs

• M:F ratio 2:1

• Pathology: indentation involving anterior, lateral &
  posterior wall of aorta

 Postductal type: distal to ductus/ ligamentum
 arteriosum or subclavian artery -adult type

 Preductal-proximal (infantile)
Coarctation of the Aorta
•   Localized narrowing of the aorta
•   M>F
•   Associated with Turner’s Syndrome
•   Most common clinical sign: weak pulses &
    decreased blood pressure in the lower extremities
Coarctation of Aorta
Hemodynamics:
• Preductal type: very high load on left ventricle
  elevation of both systolic & diastolic pressures
  absence of collaterals immediately symptomatic
  with CCF from birth

• Postductal type: development of collaterals
  connecting branches of subclavian artery to arteries
  arising from aorta from in-utero life distal level of
  coarctation spares infant from LVF
Clinical manifestations:
• Symptomatic infants-
   H/O poor feeding, dyspnea, poor weight gain,
  signs of acute circulatory shock in first 6 weeks
  of life

• Weakness or pain in legs after exertion
Clinical manifestations:
• Intermittent claudication

• Dyspnea on running

• Physical examination: pale, respiratory
  distress, weak femoral pulses, radio-femoral
  delay, BP in arms more than in legs
Precordial examination
Heart size N – apex normal site but heaving
• Systolic thrill in suprasternal notch
• S1 – accentuated with constant ejection click
• S2 – normally split with loud A2
• Murmur - ejection systolic murmur grade 2-4/6
  at URSB & mid or lower left sternal border,
  systolic murmur at interscapular area (left)
Diagnosis:
•   CXR: heart size N with prominent ascending
        aorta and aortic knuckle
        “3” sign on over-penetrated films
        rib notching between 4th and 8th ribs

•   “E” sign on barium swallow

•   ECG: left axis deviation, LVH

•   Echo: coarctation visualized
Management:
• Medical: control of CCF in infancy
        dental hygiene
       Infective endocarditis prophylaxis
       Treat HTN
       Balloon angioplasty

• Surgical: resection of coarctation and end-to-end
  anastomosis at any age but lowest risk at 1-10yrs
Thank you
Download more documents and slide shows on The Medical Post
               [ www.themedicalpost.net ]

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Coarctation of Aorta

  • 1. Coarctation of Aorta Dr. Kalpana Malla MBBS MD (Pediatrics) Manipal Teaching Hospital Download more documents and slide shows on The Medical Post [ www.themedicalpost.net ]
  • 2. Coarctation of aorta • 8-10% of CHDs • M:F ratio 2:1 • Pathology: indentation involving anterior, lateral & posterior wall of aorta  Postductal type: distal to ductus/ ligamentum arteriosum or subclavian artery -adult type  Preductal-proximal (infantile)
  • 3. Coarctation of the Aorta • Localized narrowing of the aorta • M>F • Associated with Turner’s Syndrome • Most common clinical sign: weak pulses & decreased blood pressure in the lower extremities
  • 5. Hemodynamics: • Preductal type: very high load on left ventricle elevation of both systolic & diastolic pressures absence of collaterals immediately symptomatic with CCF from birth • Postductal type: development of collaterals connecting branches of subclavian artery to arteries arising from aorta from in-utero life distal level of coarctation spares infant from LVF
  • 6. Clinical manifestations: • Symptomatic infants- H/O poor feeding, dyspnea, poor weight gain, signs of acute circulatory shock in first 6 weeks of life • Weakness or pain in legs after exertion
  • 7. Clinical manifestations: • Intermittent claudication • Dyspnea on running • Physical examination: pale, respiratory distress, weak femoral pulses, radio-femoral delay, BP in arms more than in legs
  • 8. Precordial examination Heart size N – apex normal site but heaving • Systolic thrill in suprasternal notch • S1 – accentuated with constant ejection click • S2 – normally split with loud A2 • Murmur - ejection systolic murmur grade 2-4/6 at URSB & mid or lower left sternal border, systolic murmur at interscapular area (left)
  • 9. Diagnosis: • CXR: heart size N with prominent ascending aorta and aortic knuckle “3” sign on over-penetrated films rib notching between 4th and 8th ribs • “E” sign on barium swallow • ECG: left axis deviation, LVH • Echo: coarctation visualized
  • 10. Management: • Medical: control of CCF in infancy dental hygiene Infective endocarditis prophylaxis Treat HTN Balloon angioplasty • Surgical: resection of coarctation and end-to-end anastomosis at any age but lowest risk at 1-10yrs
  • 11. Thank you Download more documents and slide shows on The Medical Post [ www.themedicalpost.net ]