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EAR

DEVELOPMENT
DEVELOPMENT OF EAR
EXTERNAL EAR
SOUND COLLECTING ORGAN
MIDDLE EAR
SOUND CONDUCTING ORGAN
INTERNAL EAR
CONVERTS SOUND WAVES INTO NERVE IMPULSE
CONTAINS VESTIBULOCOCHLEAR ORGAN
CONCERNED WITH EQUILIBRIUM AND HEARING
DEVELOPMENT OF INTERNAL EAR
1---OTIC PLACODE—THICKENING OF ECTODERM
ON EACH SIDE OF RHOMBENCEPHALON
INVAGINATES AND FORMS---
2---OTIC PIT
3---OTIC VESICLE/OTOCYST
    PRIMORDIUM OF MEMBRANOUS LABYRINTH
DEVELOPMENT OF INTERNAL EAR
OTIC VESICLE
1---VENTRAL COMPONENT
    a—SACCULE
    b---COCHLEAR DUCT
2---DORSAL COMPONENT
    a---UTRICLE
    b---SEMICIRCULAR CANALS
    c ---ENDOLYMPHATIC DUCT—A DIVERTICULUM
         FROM THE VESICLE
DEVELOPMENT OF INTERNAL EAR
• STATOACCOUSTIC GANGLION
• GROUP OF CELLS WHICH BREAKS AWAY
  FROM THE OTIC VESICLE
• ALSO RECEIVES CELLS FROM NEURAL CREST
• SPLITS INTO---1—COCHLEAR PART
•               ---2---VESTIBULAR PART
DEVELOPMENT OF INTERNAL EAR
COCHLEAR AND VESIBULAR PARTS SUPPLY THE
SENSORY CELLS OF—
1—ORGAN OF CORTI
2---SACCULE
3---UTRICLE
4---SEMICIRCULAR CANALS
DEVELOPMENT OF INTERNAL EAR
• SACCULE COCHLEA AND ORGAN OF CORTI
• TUBULAR OUTPOCKETING FROM THE LOWER
  END OF SACCULE– THE COCHLEAR DUCT
• APPEARS IN THE 6th WEEK
• PENETERATES THE SURROUNDNG MESENCHYME
  IN A SPIRAL FASHION

• COMPLETES 2.5 TURNS AT THE END OF 8th WEEK
• FORMS THE MEMBRANOUS COCHLEA
DEVELOPMENT OF INTERNAL EAR
SACCULE [ CONTD ]
CONNECTION OF COCH DUCT WITH THE
SACCULE IS REDUCED TO A NARROW DUCTUS
REUNIENS
MESENCHYME SURROUNDING THE COHLEAR
DUCT DIFFERENTIATES INTO CARTILAGENOUS
OTIC CAPSULE
DEVELOPMENT OF INTERNAL EAR
• MEMBRANOUS LABYRINTH ENLARGES AND
  VACUOLES APPEAR IN CARTILAGENOUS
  CAPSULE IN THE 10th WEEK
• VACUOLES BECOME CONFLUENT TO FORM
  PERILYMPHATIC SPACE
• MEMBRANOUS LABYRINTH SUSPENDED IN A
  FLUID [ PERILYMPH ] IN THE PERILYMPHATIC
  SPACE
• CARTILAGENOUS CAPSULE OSSIFIES TO FORM THE
  BONY LABYRINTH
DEVELOPMENT OF INTERNAL EAR
PERILYMPHATIC SPACE RELATED TO COCHLEAR
DUCT DEVELOPS INTO---
1—SCALA VESTIBULI SEPARATED FROM THE
     COCHLEA BY THE VESTIBULAR MEMBRANE
2---SCLA TYMPANI SEPARATED FROM THE
    COCHLEA BY THE BASILAR MEMBRANE
LAT WALL OF COCH DUCT REMAINS ATTACHED
TO THESURROUNDING CARTILAGE BY SPIRAL
 LIGAMENT
MEDIAN ANGLE OF COCH. DUCT IS CONNECTED TO AND
 IS SUPPORTED BY A LONG CARTILAGENOUS PROCESS—THE
MODIOLUS FUTURE AXIS OF COCHLEA
DEVELOPMENT OF INTERNAL EAR
SPIRAL ORGAN OF CORTI
DIFFERENTIATES FROM CELLS IN THE WALLS OF
COCHLEAR DUCT
GANGLION CELLS OF 8th NERVE MIGRATE ALONG
THE COILS OF COCHLEA
FORMS THE SPIRAL GANGLION
NERVE PROCESSES EXTEND FROM THE
GANGLION TO THE SPIRAL ORGAN WHERE THEY
TERMINATE ON THE HAIR CELLS
DEVELOPMENT OF INTERNAL EAR
SPIRAL ORGAN OF CORTI
EPITHELIAL CELLS OF THE COCHLEA FORM TWO
RIDGES---
1—INNER RIDGE [SPIRAL LIMBUS ]
2---OUTER RIDGE
OUTER RIDGE FORMS 3—4 ROWS OF HAIR
CELLS—SENSORY CELLS OF AUDITORY SYSTEM
HAIR CELLS COVERED BY TECTORIAL MEMBRANE
DEVELOPMENT OF INTERNAL EAR
ORGAN OF CORTI [CONTD]
TECTORIAL MEMBRANE IS ATTACHED TO SPIRAL
LIMBUS AND ITS TIP IS ON HAIR CELLS
ORGAN OF CORTI FORMED BY—1-TECT MEMB
                           ---2-HAIR CELLS
IMPULSES RECEIVED BY THE ORGAN OF CORTI
ARE TRANSMITTED TO---SPIRAL GANGLION
FROM THERE TO CNS BY THE AUDITORY FIBRES
OF 8TH CRANIAL NERVE
DEVELOPMENT OF INTERNAL EAR
UTRICLE AND SEMICIRCULAR CANALS
SEMICIRCULAR CANALS APPEAR AS FLAT
OUTPOCKETINGS OF THE UTRICLE
CENTRAL PORTIONS OF THE WALLS OF THESE
DISAPPEAR FORMING 3 SEMICIRCULAR CANALS
1—POSTERIOR
2—SUPERIOR/ANTERIOR
3—LATERAL/HORIZONTAL
DEVELOPMENT OF INTERNAL EAR
SEMICIRCULAR CANALS[CONTD]
ONE END OF EACH CANAL DILATES TO FORM
CRUS AMPULLARES
IMPULSE GENERATED IN SENSORY CLLS OF
CRISTAE AND MACULAE AS A RESULT OF
CHANGE IN POSITON ARE TRANSMITTED BY
VESTIBULAR FIBRES
DEVELOPMENT OF INTERNAL EAR
MACULAE ARE SENSORY AREAS IN THE WALLS
OF UTRICLE AND SACCULE

CELLS IN THE AMPULLAE FORM A CREST----
CRISTA AMPULLARIS CONTAINING SENSORY
CELLS FOR THE MAINTENANCE OF EQUILIBRIUM
DEVELOPMENT OF MIDDLE EAR
TYMPANIC CAVITY AND AUDITORY TUBE
• TYMPANIC CAVITY DERIVED FROM THE ENDODERM OF
  1st PHARYNGEAL POUCH
• POUCH EXPANDS LATERALLY
• COMES INTO CONTACT WITH 1st PHARYNGEAL
  CLEFT
• DISTAL PART FORMS TUBOTYMPANIC RECESS
• WIDENS AND FORMS THE TYMPANIC CAVITY
• PROXIMAL PART REMAINS NARROW AND FORMS THE
  AUDITORY TUBE THROUGH WHICH TYMP CAVITY
  COMMUNICATES WITH THE NASOPHARYNX
DEVELOPMENT OF MIDDLE EAR
OSSICLES
MALLEUS AND INCUS FROM THE CARTILAGE OF
1st ARCH
STAPES FROM THE CARTILAGE OF 2nd ARCH
REMAIN EMBEDDED IN THE SURROUNDING
MESENCHYME TILL THE 8th MONTH
OSSICLES ARE FREE WHEN THE MESENCHYME
DISSOLVES
DEVELOPMENT OF MIDDLE EAR
OSSICLES [CONTD ]
WHEN FREE BECOME SURROUNDED BY THE
ENDODERMAL EPITHELIUM OF TYMPANIC
CAVITY
EPITHELIUM CONNECTS THEM TO THE WALL OF
THE CAVITY
SUPPORTING LIGAMENTS DEVELOP LATER
DEVELOPMENT OF MIDDLE EAR
MASTOID PROCESS
DURING LATE FOETAL LIFE TYMP CAVITY
EXPANDS TO FORM MASTOID ANTRUM
LOCATED IN THE PETROMASTOID PART OF
TEMPORAL BONE
AFTER BIRTH EPITHELIUM OF TYMPANIC CAVITY
INVADES THE DEVELOPING MASTOID PROCESS
LATER EPITHELIUM LINED SACS ARE FORMED
MIDDLE EAR CONTINUES TO GROW THROUGH
PUBERTY
DEVELOPMENT OF EXTERNAL EAR
EXTERNAL AUDITORY MEATUS
• FROM THE DORSAL PART OF 1st PHARYNGEAL
  GROOVE
• ECTODERMAL CELLS AT THE BOTTOM OF THIS
  FUNNEL SHAPED TUBE PROLIFERATE TO FORM
  MEATAL PLUG
• IN LATE FOETAL PERIOD CENTRAL CELLS
  DEGENERATE
• MEATUS RELATIVELY SHORT AT BIRTH
• ATTAINS ADULT LENGTH AROUND 9th YEAR
DEVELOPMENT OF EXTERNAL EAR
TYMPANIC MEMBRANE
SOURCES
1st PHARYNGEAL MEMBRANE
EXTERNAL COVERING FROM SURFACE
ECTODERM
INTERNAL COVERING FROM ENDODERM OF
TUBOTYMPANIC RECESS
MESODERM OF Ist &2nd ARCH GROWS B/W THE
TWO LAYERS AND FORMS THE FIBROUS STRATUM
MAJOR PART OF THE MEMB FIRMLY ATTACHED TO THE
 HANDLE OF MALLEUS
DEVELOPMENT OF EXTERNAL EAR
AURICLE
SOURCE
SIX MESENCHYMAL SWELLINGS ----
AURICULAR HILLOCKS
ARISE ALONG THE MARGIN OF 1st GROOVE
FUSE AND FORM THE DEFINITIVE AURICLE
CONGENITAL ANOMALIES OF EAR
1---CONGENITAL DEAFNESS---
    a—CONDUCTIVE
    b---NERVE
CAUSES
1--MOSTLY GENETIC FACTORS
2--MAY BE ASSOCIATED WITH OTHER HEAD AND
NECK ABNORMALITIES
3 1st ARCH SYNDROME—INCUS &MALLEUS
  INVOLVED
CONGENITAL ANOMALIES OF EAR
CONGENITAL DEAFNESS [CONTD ]
4--RUBELLA DURING 7th & 8th WEEK MAY CAUSE
MALDEVELOPMENT OF SPIRAL ORGAN
5--MATERNAL GOITER
6--CONGENITAL FIXATION OF THE STAPES
CONGENITAL ANOMALIES OF EAR
AURICILAR ABNORMALITIES [ COSMETIC ]
1—PREAURICULAR SINUS—PIT LIKE CUTANEOUS
  DEPRESSION—TRIANGULAR AREA ANTERIOR
  TO THE AURICLE
  CAUSE? ABNORMAL DEVELOPMENT OF
  HILLOCKS
  FAMILIAL AND OFTEN BILATERAL
CONGENITAL ANOMALIES OF EAR
2—AURICULAR APPENDAGES
  CAUSE—DUE TO FORMATION OF ACCESSORY
  HILLOCKS
  USUALLY ANTERIOR TO AURICLE
  MORE OFTEN UNILATERAL
CONGENITAL ANOMALIES OF EAR
3—ANOTIA
  ABSENCE OF AURICLE
  COMMONLY ASSOCIATED WITH 1st ARCH SYN
4—MICROTIA
  SMALL AURICLE
5—ATRESIA OF EXT ACCOUSTIC MEATUS
  FAILURE OF MEATAL PLUG TO CANALIZE
CONGENITAL ANOMALIES OF EAR
6—CONGENITAL CHOLESTEATOMA
   REST OF EPITHELIAL CELLS
   APPEAR AS WHITE CYST LIKE STRUCTURES
   MEDIAL TO OR WITHIN THE TYMPANIC
   MEMBRANE
   ORIGIN FROM MEATAL PLUG
REST---GROUP OF CELLS THAT HAVE BECOME
DISPLACED AND LIES IN TISSUE OF ANOTHER
CHARACTER

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The cerebellum demoThe cerebellum demo
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Structural organization of nervous system new
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Speech
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Scalp
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Dorsal column pathway
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Treatment of parknsonism
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Tousif, role of receptors
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Triangles of the neck ppt year 1
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cranial nerves 2 and 3
cranial nerves 2 and 3cranial nerves 2 and 3
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Cranial nerve ix , xii
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Cranial nerve iii , iv and vi
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Ear final

  • 2. DEVELOPMENT OF EAR EXTERNAL EAR SOUND COLLECTING ORGAN MIDDLE EAR SOUND CONDUCTING ORGAN INTERNAL EAR CONVERTS SOUND WAVES INTO NERVE IMPULSE CONTAINS VESTIBULOCOCHLEAR ORGAN CONCERNED WITH EQUILIBRIUM AND HEARING
  • 3. DEVELOPMENT OF INTERNAL EAR 1---OTIC PLACODE—THICKENING OF ECTODERM ON EACH SIDE OF RHOMBENCEPHALON INVAGINATES AND FORMS--- 2---OTIC PIT 3---OTIC VESICLE/OTOCYST PRIMORDIUM OF MEMBRANOUS LABYRINTH
  • 4.
  • 5.
  • 6. DEVELOPMENT OF INTERNAL EAR OTIC VESICLE 1---VENTRAL COMPONENT a—SACCULE b---COCHLEAR DUCT 2---DORSAL COMPONENT a---UTRICLE b---SEMICIRCULAR CANALS c ---ENDOLYMPHATIC DUCT—A DIVERTICULUM FROM THE VESICLE
  • 7.
  • 8. DEVELOPMENT OF INTERNAL EAR • STATOACCOUSTIC GANGLION • GROUP OF CELLS WHICH BREAKS AWAY FROM THE OTIC VESICLE • ALSO RECEIVES CELLS FROM NEURAL CREST • SPLITS INTO---1—COCHLEAR PART • ---2---VESTIBULAR PART
  • 9. DEVELOPMENT OF INTERNAL EAR COCHLEAR AND VESIBULAR PARTS SUPPLY THE SENSORY CELLS OF— 1—ORGAN OF CORTI 2---SACCULE 3---UTRICLE 4---SEMICIRCULAR CANALS
  • 10. DEVELOPMENT OF INTERNAL EAR • SACCULE COCHLEA AND ORGAN OF CORTI • TUBULAR OUTPOCKETING FROM THE LOWER END OF SACCULE– THE COCHLEAR DUCT • APPEARS IN THE 6th WEEK • PENETERATES THE SURROUNDNG MESENCHYME IN A SPIRAL FASHION • COMPLETES 2.5 TURNS AT THE END OF 8th WEEK • FORMS THE MEMBRANOUS COCHLEA
  • 11.
  • 12. DEVELOPMENT OF INTERNAL EAR SACCULE [ CONTD ] CONNECTION OF COCH DUCT WITH THE SACCULE IS REDUCED TO A NARROW DUCTUS REUNIENS MESENCHYME SURROUNDING THE COHLEAR DUCT DIFFERENTIATES INTO CARTILAGENOUS OTIC CAPSULE
  • 13. DEVELOPMENT OF INTERNAL EAR • MEMBRANOUS LABYRINTH ENLARGES AND VACUOLES APPEAR IN CARTILAGENOUS CAPSULE IN THE 10th WEEK • VACUOLES BECOME CONFLUENT TO FORM PERILYMPHATIC SPACE • MEMBRANOUS LABYRINTH SUSPENDED IN A FLUID [ PERILYMPH ] IN THE PERILYMPHATIC SPACE • CARTILAGENOUS CAPSULE OSSIFIES TO FORM THE BONY LABYRINTH
  • 14. DEVELOPMENT OF INTERNAL EAR PERILYMPHATIC SPACE RELATED TO COCHLEAR DUCT DEVELOPS INTO--- 1—SCALA VESTIBULI SEPARATED FROM THE COCHLEA BY THE VESTIBULAR MEMBRANE 2---SCLA TYMPANI SEPARATED FROM THE COCHLEA BY THE BASILAR MEMBRANE LAT WALL OF COCH DUCT REMAINS ATTACHED TO THESURROUNDING CARTILAGE BY SPIRAL LIGAMENT MEDIAN ANGLE OF COCH. DUCT IS CONNECTED TO AND IS SUPPORTED BY A LONG CARTILAGENOUS PROCESS—THE MODIOLUS FUTURE AXIS OF COCHLEA
  • 15.
  • 16. DEVELOPMENT OF INTERNAL EAR SPIRAL ORGAN OF CORTI DIFFERENTIATES FROM CELLS IN THE WALLS OF COCHLEAR DUCT GANGLION CELLS OF 8th NERVE MIGRATE ALONG THE COILS OF COCHLEA FORMS THE SPIRAL GANGLION NERVE PROCESSES EXTEND FROM THE GANGLION TO THE SPIRAL ORGAN WHERE THEY TERMINATE ON THE HAIR CELLS
  • 17. DEVELOPMENT OF INTERNAL EAR SPIRAL ORGAN OF CORTI EPITHELIAL CELLS OF THE COCHLEA FORM TWO RIDGES--- 1—INNER RIDGE [SPIRAL LIMBUS ] 2---OUTER RIDGE OUTER RIDGE FORMS 3—4 ROWS OF HAIR CELLS—SENSORY CELLS OF AUDITORY SYSTEM HAIR CELLS COVERED BY TECTORIAL MEMBRANE
  • 18.
  • 19. DEVELOPMENT OF INTERNAL EAR ORGAN OF CORTI [CONTD] TECTORIAL MEMBRANE IS ATTACHED TO SPIRAL LIMBUS AND ITS TIP IS ON HAIR CELLS ORGAN OF CORTI FORMED BY—1-TECT MEMB ---2-HAIR CELLS IMPULSES RECEIVED BY THE ORGAN OF CORTI ARE TRANSMITTED TO---SPIRAL GANGLION FROM THERE TO CNS BY THE AUDITORY FIBRES OF 8TH CRANIAL NERVE
  • 20. DEVELOPMENT OF INTERNAL EAR UTRICLE AND SEMICIRCULAR CANALS SEMICIRCULAR CANALS APPEAR AS FLAT OUTPOCKETINGS OF THE UTRICLE CENTRAL PORTIONS OF THE WALLS OF THESE DISAPPEAR FORMING 3 SEMICIRCULAR CANALS 1—POSTERIOR 2—SUPERIOR/ANTERIOR 3—LATERAL/HORIZONTAL
  • 21.
  • 22. DEVELOPMENT OF INTERNAL EAR SEMICIRCULAR CANALS[CONTD] ONE END OF EACH CANAL DILATES TO FORM CRUS AMPULLARES IMPULSE GENERATED IN SENSORY CLLS OF CRISTAE AND MACULAE AS A RESULT OF CHANGE IN POSITON ARE TRANSMITTED BY VESTIBULAR FIBRES
  • 23. DEVELOPMENT OF INTERNAL EAR MACULAE ARE SENSORY AREAS IN THE WALLS OF UTRICLE AND SACCULE CELLS IN THE AMPULLAE FORM A CREST---- CRISTA AMPULLARIS CONTAINING SENSORY CELLS FOR THE MAINTENANCE OF EQUILIBRIUM
  • 24. DEVELOPMENT OF MIDDLE EAR TYMPANIC CAVITY AND AUDITORY TUBE • TYMPANIC CAVITY DERIVED FROM THE ENDODERM OF 1st PHARYNGEAL POUCH • POUCH EXPANDS LATERALLY • COMES INTO CONTACT WITH 1st PHARYNGEAL CLEFT • DISTAL PART FORMS TUBOTYMPANIC RECESS • WIDENS AND FORMS THE TYMPANIC CAVITY • PROXIMAL PART REMAINS NARROW AND FORMS THE AUDITORY TUBE THROUGH WHICH TYMP CAVITY COMMUNICATES WITH THE NASOPHARYNX
  • 25.
  • 26. DEVELOPMENT OF MIDDLE EAR OSSICLES MALLEUS AND INCUS FROM THE CARTILAGE OF 1st ARCH STAPES FROM THE CARTILAGE OF 2nd ARCH REMAIN EMBEDDED IN THE SURROUNDING MESENCHYME TILL THE 8th MONTH OSSICLES ARE FREE WHEN THE MESENCHYME DISSOLVES
  • 27. DEVELOPMENT OF MIDDLE EAR OSSICLES [CONTD ] WHEN FREE BECOME SURROUNDED BY THE ENDODERMAL EPITHELIUM OF TYMPANIC CAVITY EPITHELIUM CONNECTS THEM TO THE WALL OF THE CAVITY SUPPORTING LIGAMENTS DEVELOP LATER
  • 28.
  • 29. DEVELOPMENT OF MIDDLE EAR MASTOID PROCESS DURING LATE FOETAL LIFE TYMP CAVITY EXPANDS TO FORM MASTOID ANTRUM LOCATED IN THE PETROMASTOID PART OF TEMPORAL BONE AFTER BIRTH EPITHELIUM OF TYMPANIC CAVITY INVADES THE DEVELOPING MASTOID PROCESS LATER EPITHELIUM LINED SACS ARE FORMED MIDDLE EAR CONTINUES TO GROW THROUGH PUBERTY
  • 30.
  • 31.
  • 32. DEVELOPMENT OF EXTERNAL EAR EXTERNAL AUDITORY MEATUS • FROM THE DORSAL PART OF 1st PHARYNGEAL GROOVE • ECTODERMAL CELLS AT THE BOTTOM OF THIS FUNNEL SHAPED TUBE PROLIFERATE TO FORM MEATAL PLUG • IN LATE FOETAL PERIOD CENTRAL CELLS DEGENERATE • MEATUS RELATIVELY SHORT AT BIRTH • ATTAINS ADULT LENGTH AROUND 9th YEAR
  • 33. DEVELOPMENT OF EXTERNAL EAR TYMPANIC MEMBRANE SOURCES 1st PHARYNGEAL MEMBRANE EXTERNAL COVERING FROM SURFACE ECTODERM INTERNAL COVERING FROM ENDODERM OF TUBOTYMPANIC RECESS MESODERM OF Ist &2nd ARCH GROWS B/W THE TWO LAYERS AND FORMS THE FIBROUS STRATUM MAJOR PART OF THE MEMB FIRMLY ATTACHED TO THE HANDLE OF MALLEUS
  • 34. DEVELOPMENT OF EXTERNAL EAR AURICLE SOURCE SIX MESENCHYMAL SWELLINGS ---- AURICULAR HILLOCKS ARISE ALONG THE MARGIN OF 1st GROOVE FUSE AND FORM THE DEFINITIVE AURICLE
  • 35.
  • 36. CONGENITAL ANOMALIES OF EAR 1---CONGENITAL DEAFNESS--- a—CONDUCTIVE b---NERVE CAUSES 1--MOSTLY GENETIC FACTORS 2--MAY BE ASSOCIATED WITH OTHER HEAD AND NECK ABNORMALITIES 3 1st ARCH SYNDROME—INCUS &MALLEUS INVOLVED
  • 37. CONGENITAL ANOMALIES OF EAR CONGENITAL DEAFNESS [CONTD ] 4--RUBELLA DURING 7th & 8th WEEK MAY CAUSE MALDEVELOPMENT OF SPIRAL ORGAN 5--MATERNAL GOITER 6--CONGENITAL FIXATION OF THE STAPES
  • 38. CONGENITAL ANOMALIES OF EAR AURICILAR ABNORMALITIES [ COSMETIC ] 1—PREAURICULAR SINUS—PIT LIKE CUTANEOUS DEPRESSION—TRIANGULAR AREA ANTERIOR TO THE AURICLE CAUSE? ABNORMAL DEVELOPMENT OF HILLOCKS FAMILIAL AND OFTEN BILATERAL
  • 39. CONGENITAL ANOMALIES OF EAR 2—AURICULAR APPENDAGES CAUSE—DUE TO FORMATION OF ACCESSORY HILLOCKS USUALLY ANTERIOR TO AURICLE MORE OFTEN UNILATERAL
  • 40.
  • 41. CONGENITAL ANOMALIES OF EAR 3—ANOTIA ABSENCE OF AURICLE COMMONLY ASSOCIATED WITH 1st ARCH SYN 4—MICROTIA SMALL AURICLE 5—ATRESIA OF EXT ACCOUSTIC MEATUS FAILURE OF MEATAL PLUG TO CANALIZE
  • 42.
  • 43.
  • 44. CONGENITAL ANOMALIES OF EAR 6—CONGENITAL CHOLESTEATOMA REST OF EPITHELIAL CELLS APPEAR AS WHITE CYST LIKE STRUCTURES MEDIAL TO OR WITHIN THE TYMPANIC MEMBRANE ORIGIN FROM MEATAL PLUG REST---GROUP OF CELLS THAT HAVE BECOME DISPLACED AND LIES IN TISSUE OF ANOTHER CHARACTER