28. Concentrations of proteins important in coagulation in the nephrotic syndrome in relation to molecular weight Reduced 54,000 α 1 -Antitrypsin Raised–normal 65,000 Protein C Normal–reduced 68,000 Antithrombin III Normal–reduced 70,000 α 2 -Antiplasmin Normal–reduced 75,000 Protein S Normal–reduced 81,000 Plasminogen Raised 840,000 α 1 -Macroglobulin Regulator proteins Normal–reduced 55,400 Factor IX Normal–reduced 56,000 Factor X Normal–reduced 72,000 Factor II (prothrombin) Normal–reduced 79,000 Factor XII Normal–reduced 160,000 Factor XI Raised–normal 200,000 Factor VII Raised 330,000 Factor I (fibrinogen) Raised 350,000 Factor V Raised 840,000 Von Willebrand factor Zymogens and cofactors Concentration in nephrotic plasma MW (Da) Protein